منابع مشابه
Megacystis Megacolon Intestinal Hypoperistalsis Syndrome: A Rare Entity!
Megacystis microcolon intestinal hypoperistalsis syndrome (MMIHS) is now a well established entity [1,2]. Also known as Berdon syndrome [1], it is characterized by massive abdominal distension caused by a largely dilated non obstructed urinary bladder, microcolon and decreased or absent intestinal peristalsis. Isolated cases of congenital megacystis [3,4] and microcolon without megacystis [5] h...
متن کاملIdiopathic megarectum and megacolon.
A 56-year-old female with a prior medical history of congenital mental retardation, hypercholesterolemia, and hypothyroidism consulted for severe constipation refractory to laxatives, which required enemas for evacuation, associated with abdominal distension and weight loss –8 kg over the last six months–. Physical examination revealed a hard, long, rounded mass measuring 8 x 10 cm in the centr...
متن کاملA Case of Megacolon
Megacolon is a relatively rare condition appearing in childhood and characterised by obstinate constipation, dilatation of the colon and hypomotility of its wall. It was Yon Ammon who first described megacolon in 1842, fortyfive years before Hirschsprung, though the disease carries the name of the latter. Since then many {etiological factors have been considered, ranging from malnutrition to ne...
متن کاملMegacystis-Microcolon-Intestinal Hypoperistalsis Syndrome (MMIHS).
Introduction Megacystismicrocolon -intestinal hypoperistalsis syndrome(MMIHS) also called as BERDON SYNDROME is a rare congenital disease characterized by massive abdominal distension caused by a largely dilated non-obstructed urinary bladder, microcolon and decreased or absent intestinal peristalsis. It poses a diagnostic and therapeutic challenge to the surgeon. It the most severe form of fun...
متن کاملMegacystis-Microcolon-Intestinal Hypoperistalsis Syndrome
We report a case of megacystis-microcolon-intestinal hypoperistalsis syndrome (MMIHS) in a newborn female infant who presented with an abdominal mass, absent bowel sounds, and feeding intolerance with bilious emesis. MMIHS is a rare congenital bowel and bladder defect requiring surgery and chronic total parenteral nutrition in an attempt to sustain life. With few exceptions, it is predominately...
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ژورنال
عنوان ژورنال: Archives of Pediatrics & Adolescent Medicine
سال: 1915
ISSN: 1072-4710
DOI: 10.1001/archpedi.1915.04100460024002